RareResearch.AI
← Back to atlas

G831D

Category 3/4 — Most DruggableConflictingLumenal · predictedσ-1 candidateEditorial
GlycineAspartate at position 831 · C-terminal lumenal domain (653-869) · WFS1 (Wolframin)

Glycine → Aspartate at position 831 in wolframin's C-terminal lumenal domain. ClinVar Conflicting. AlphaMissense 0.923, ΔΔG -0.85. Glycine-removal with charge introduction.

Interactive 3D Structure

Wild-type reference
Wild-type G831 — hydrogen bond to L833
Fullscreen ↗
DynaMut2 mutant · G831D
Mutant D831 — energy-minimized; local contact network preserved
Fullscreen ↗

Bond changes · DynaMut2 interaction analysis

0 lost0 gained3 preserved
Interaction typeWild-type partnerMutant partnerStatus
Hydrogen bondL833L833Preserved
Polar contactL833L833Preserved
Van der WaalsL833L833Preserved

Lost / gained / preserved interatomic contacts at the variant residue, from the DynaMut2 (Arpeggio) interaction analysis of the wild-type and energy-minimized mutant structures.

Computational Predictions

DynaMut2 ΔΔG
-0.85kcal/mol
Destabilising — mild
AlphaMissense
0.923
LPath
AlphaFold pLDDT
78
model confidence
Schema
Cat 3/4
Category 3/4 — Most Druggable
ΔΔG confidence: Standard confidence · Lumenal

This variant is in a water-facing region, which is the regime the stability predictor was built and benchmarked for. Ordinary predictor error still applies.

Clinical Evidence

ClinVar classificationConflicting classifications of pathogenicity
Review statuscriteria provided, conflicting classifications
Associated conditions(no specific conditions catalogued)
InheritanceNot specified.
Population frequency (gnomAD v4)Ultra-rare · AF 0.00062%
cDNA changec.2492G>A
ClinVar accessionVCV000004523
Last evaluated2026/02/04 00:00

Observed at very low frequency in gnomAD.

Classified for1★ unverified submission

ClinVar classifies this variant as Conflicting classifications of pathogenicity, but does not state what it is classified for. ClinVar records the condition only as "not provided". A classification without a phenotype and an inheritance mode cannot be read as a statement about Wolfram syndrome risk or severity.

  • Phenotype scope is interpretation of submitted records. The computed values on this card (AlphaMissense, DynaMut2 ΔΔG, pLDDT) are measurements of the model, not of a patient.
  • Presentation cannot be generalised from neighbouring variants: one nucleotide over can present very differently. Structural similarity supports a mechanistic hypothesis, never a phenotype claim.

Review status: 1★ conflicting classifications. ClinVar "conditions" is the union of all submissions; 0–1★ entries are submitted conditions, not documented phenotypes.

Population frequency
Global (all ancestries)
AF 0.00062% · 10 / 1,604,952 alleles
Homozygotes
0
Highest-frequency population
European (non-Finnish) · AF 0.00085%

Highest in European (non-Finnish): AF 0.00085% (10 of 1,174,140 alleles), in line with the global figure.

No homozygotes reported in gnomAD v4. For a recessive allele this is expected and is not, on its own, evidence either way.

Ancestry groupAllele freq.AC / ANHom.Carrier est.
European (non-Finnish)0.00085%10 / 1,174,1400~1 in 58710

Source: gnomAD r4, retrieved 2026-08-21. Values are allele frequencies. The carrier estimate is derived from the allele frequency (Hardy-Weinberg, ~2·AF) and is an approximation, not a published figure — where a published carrier frequency exists it outranks this column and is cited on the card.

Structural Context

Position 831 sits in the lumenal domain. Neighbors: ARG832 (2.5 Å — likely salt-bridge partner with new D831!), GLU830 (2.5 Å — adjacent existing carboxylate), LEU833 (4.7 Å), GLU694 (4.8 Å — long-range).

Replacing G831 with aspartate creates a charge cluster: the new D831 carboxylate plus the existing E830, with R832 nearby as potential bridge. The local backbone flexibility is lost; the local electrostatic environment is transformed.

The |ΔΔG| of 0.85 reflects substantial fold cost. AlphaMissense 0.923 confirms severe consequence.

Amino-acid chemistry
Glycine (G) → Aspartate (D) — smallest amino acid replaced by negatively-charged carboxylate. Loss of backbone flexibility plus charge introduction.
Position in the protein
C-terminal lumenal domain · position 831 (pLDDT 78).

Druggability Assessment

Category 3/4 — Most Druggable. |ΔΔG| = 0.85 — fold survives. AlphaMissense 0.923 confirms severe consequence.

Mechanism: glycine-removal plus charge introduction at the R832-E830 electrostatic environment. Therapeutic: site-directed at the 830-832 microregion.

Why this matters

G831D continues the glycine-removal class — universally pathogenic across the Atlas.
Therapeutic Strategy Handoff · prediction

Feed this card to Wolfram Intelligence

Download the G831D PDF below and upload it to Wolfram Intelligence to generate therapeutic-strategy proposals — guanidinium mimetics, sigma-1 agonist docking, NAC thiol-capping. NAC is already on the bench-testing list.

Download G831D PDF card ↓Strategies are AI-generated predictions, not validated therapeutics.

UniProt Domain Annotation

Chain1890 · Wolframin
Topological domain653869 · Lumenal
Natural variant831831 · in DFNA6; dbSNP:rs28937895