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V415F

Category 3/4 — Most DruggableLikely pathogenicTransmembrane · predictedEditorial
ValinePhenylalanine at position 415 · TM3 (402-422), helical transmembrane · WFS1 (Wolframin)

Valine → Phenylalanine at position 415 inside TM3. ClinVar Likely pathogenic, Cataract 41. AlphaMissense 0.574 (just above threshold), DynaMut2 ΔΔG -1.64 kcal/mol (destabilising) — close to Cat 2. Volume increase in TM3.

Interactive 3D Structure

Wild-type reference
Wild-type V415 — hydrogen bond to F419
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DynaMut2 mutant · V415F
Mutant F415 — hydrogen bond to S418 lost (5 contacts lost)
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Bond changes · DynaMut2 interaction analysis

5 lost6 gained14 preserved
Interaction typeWild-type partnerMutant partnerStatus
Hydrogen bondM357Lost
Hydrogen bondS411S411Preserved
Hydrogen bondV412V412Preserved
Hydrogen bondS418S418Preserved
Hydrogen bondF419F419Preserved
Polar contactS353Lost
Polar contactS411S411Preserved
Polar contactV412V412Preserved
Polar contactF413F413Preserved
Polar contactF417Lost
Polar contactS418S418Preserved
Polar contactF419F419Preserved
Aromatic / πF350Gained
Aromatic / πF354Gained
Van der WaalsS353Lost
Van der WaalsF354Gained
Van der WaalsV412Gained
Van der WaalsF413Gained
Van der WaalsF417Lost
Van der WaalsF419F419Preserved
HydrophobicF350F350Preserved
HydrophobicF354F354Preserved
HydrophobicM357M357Preserved
HydrophobicL543L543Preserved
HydrophobicI547Gained

Lost / gained / preserved interatomic contacts at the variant residue, from the DynaMut2 (Arpeggio) interaction analysis of the wild-type and energy-minimized mutant structures.

Computational Predictions

DynaMut2 ΔΔG
-1.64kcal/mol
Destabilising — moderate
AlphaMissense
0.574
LPath
AlphaFold pLDDT
93
model confidence
Schema
Cat 3/4
Category 3/4 — Most Druggable
ΔΔG confidence: Reduced confidence · Transmembrane
  • transmembrane position; predictor benchmarked on soluble proteins

This variant sits in the transmembrane band. The stability value was computed with a predictor benchmarked on water-soluble proteins. Published benchmarks of ddG predictors on membrane proteins report correlation below 0.4. Treat the magnitude as unreliable and the sign as weak evidence only.

Do not rank this value against a variant from a different region on ΔΔG alone.

Clinical Evidence

ClinVar classificationLikely pathogenic
Review statusno assertion criteria provided
Associated conditionsCataract 41
InheritanceCataract 41 documented.
Population frequency (gnomAD v4)Absent from gnomAD v4
cDNA changec.1243G>T
ClinVar accessionVCV001702534
Last evaluated2022/05/26 00:00

Not observed in ~730k individuals — consistent with a rare allele (ACMG PM2_supporting).

Classified for0★ unverified submission

ClinVar classifies this variant as Likely pathogenic for Cataract 41 (autosomal dominant, OMIM 116400). These are dominant WFS1-related disorders and are clinically distinct from classic recessive Wolfram syndrome. This classification is not a statement about Wolfram syndrome severity.

  • Cataract 41autosomal dominant · OMIM 116400submitted as: Cataract 41
  • No assertion criteria were provided (0★). Treat the conditions above as unverified submissions, not as documented phenotypes.
  • Phenotype scope is interpretation of submitted records. The computed values on this card (AlphaMissense, DynaMut2 ΔΔG, pLDDT) are measurements of the model, not of a patient.
  • Presentation cannot be generalised from neighbouring variants: one nucleotide over can present very differently. Structural similarity supports a mechanistic hypothesis, never a phenotype claim.

Review status: 0★ no assertion criteria provided. ClinVar "conditions" is the union of all submissions; 0–1★ entries are submitted conditions, not documented phenotypes.

Population frequency
Global (all ancestries)
Absent from gnomAD v4
Homozygotes
Not available

No population breakdown — the variant is absent from gnomAD v4, so no ancestry group has an observed frequency.

No homozygotes — the variant is absent from gnomAD v4 altogether.

Source: gnomAD r4, retrieved 2026-08-21. Values are allele frequencies. The carrier estimate is derived from the allele frequency (Hardy-Weinberg, ~2·AF) and is an approximation, not a published figure — where a published carrier frequency exists it outranks this column and is cited on the card.

Structural Context

Position 415 sits in TM3. The AlphaFold model places V415 within 5 Å of ILE416 (2.5 Å), PHE414 (2.5 Å — already aromatic), SER418 (3.6 Å), VAL412 (3.6 Å), and SER353 (3.8 Å — TM2-TM3 cross-helix, same S353 as F350I Atlas card neighbor).

Replacing V415 with phenylalanine creates a tandem aromatic motif (F414-F415). The local TM3 packing is reorganized to accommodate the second aromatic ring. The TM2-TM3 cross-helix S353 contact (also touched by F350I) is perturbed.

The |ΔΔG| of 1.64 — close to the Cat 2 threshold — reflects substantial fold cost. AlphaMissense's 0.574 is borderline-pathogenic plus Cataract 41 clinical evidence confirms pathogenic consequence.

Amino-acid chemistry
Valine (V) → Phenylalanine (F) — small branched hydrophobic replaced by aromatic hydrophobic. Volume increases substantially.
Position in the protein
TM3 (residues 402–422) · position 415 mid-helix, bilayer-embedded (pLDDT 93 — high confidence).

Druggability Assessment

Category 3/4 — Most Druggable (near Cat 2 boundary). |ΔΔG| = 1.64 — close to Cat 2. AlphaMissense 0.574 + Cataract 41 confirm pathogenic consequence.

Mechanism is volume mismatch in TM3 plus disruption of TM2-TM3 cross-helix contact (S353). Therapeutic strategy: TM2-TM3 interface site-directed design — same target as F350I.

Why this matters

V415F + F350I both touch the S353/S418 TM2-TM3 interface — two variants converge on this previously-unidentified cross-helix target.
Therapeutic Strategy Handoff · prediction

Feed this card to Wolfram Intelligence

Download the V415F PDF below and upload it to Wolfram Intelligence to generate therapeutic-strategy proposals — guanidinium mimetics, sigma-1 agonist docking, NAC thiol-capping. NAC is already on the bench-testing list.

Download V415F PDF card ↓Strategies are AI-generated predictions, not validated therapeutics.

UniProt Domain Annotation

Chain1890 · Wolframin
Transmembrane402422 · Helical
Natural variant415415 · in WFS1; greatly reduces protein expression compared to wild-type