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V415F

Category 3/4 — Most DruggableLikely pathogenicTransmembrane · predictedEditorial
ValinePhenylalanine at position 415 · TM3 (402-422), helical transmembrane · WFS1 (Wolframin)

Valine → Phenylalanine at position 415 inside TM3. ClinVar Likely pathogenic, Cataract 41. AlphaMissense 0.574 (just above threshold), DynaMut2 ΔΔG -1.64 kcal/mol (destabilising) — close to Cat 2. Volume increase in TM3.

Interactive 3D Structure

Wild-type reference
Wild-type V415 — hydrogen bond to F419
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DynaMut2 mutant · V415F
Mutant F415 — hydrogen bond to S418 lost (5 contacts lost)
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Bond changes · DynaMut2 interaction analysis

5 lost6 gained14 preserved
Interaction typeWild-type partnerMutant partnerStatus
Hydrogen bondM357Lost
Hydrogen bondS411S411Preserved
Hydrogen bondV412V412Preserved
Hydrogen bondS418S418Preserved
Hydrogen bondF419F419Preserved
Polar contactS353Lost
Polar contactS411S411Preserved
Polar contactV412V412Preserved
Polar contactF413F413Preserved
Polar contactF417Lost
Polar contactS418S418Preserved
Polar contactF419F419Preserved
Aromatic / πF350Gained
Aromatic / πF354Gained
Van der WaalsS353Lost
Van der WaalsF354Gained
Van der WaalsV412Gained
Van der WaalsF413Gained
Van der WaalsF417Lost
Van der WaalsF419F419Preserved
HydrophobicF350F350Preserved
HydrophobicF354F354Preserved
HydrophobicM357M357Preserved
HydrophobicL543L543Preserved
HydrophobicI547Gained

Lost / gained / preserved interatomic contacts at the variant residue, from the DynaMut2 (Arpeggio) interaction analysis of the wild-type and energy-minimized mutant structures.

Computational Predictions

DynaMut2 ΔΔG
-1.64kcal/mol
Destabilising — moderate
AlphaMissense
0.574
LPath
AlphaFold pLDDT
93
model confidence
Schema
Cat 3/4
Category 3/4 — Most Druggable

Clinical Evidence

ClinVar classificationLikely pathogenic
Review statusno assertion criteria provided
Associated conditionsCataract 41
InheritanceCataract 41 documented.
Population frequency (gnomAD v4)Absent from gnomAD v4
cDNA changec.1243G>T
ClinVar accessionVCV001702534
Last evaluated2022/05/26 00:00

Not observed in ~730k individuals — consistent with a rare allele (ACMG PM2_supporting).

Structural Context

Position 415 sits in TM3. The AlphaFold model places V415 within 5 Å of ILE416 (2.5 Å), PHE414 (2.5 Å — already aromatic), SER418 (3.6 Å), VAL412 (3.6 Å), and SER353 (3.8 Å — TM2-TM3 cross-helix, same S353 as F350I Atlas card neighbor).

Replacing V415 with phenylalanine creates a tandem aromatic motif (F414-F415). The local TM3 packing is reorganized to accommodate the second aromatic ring. The TM2-TM3 cross-helix S353 contact (also touched by F350I) is perturbed.

The |ΔΔG| of 1.64 — close to the Cat 2 threshold — reflects substantial fold cost. AlphaMissense's 0.574 is borderline-pathogenic plus Cataract 41 clinical evidence confirms pathogenic consequence.

Amino-acid chemistry
Valine (V) → Phenylalanine (F) — small branched hydrophobic replaced by aromatic hydrophobic. Volume increases substantially.
Position in the protein
TM3 (residues 402–422) · position 415 mid-helix, bilayer-embedded (pLDDT 93 — high confidence).

Druggability Assessment

Category 3/4 — Most Druggable (near Cat 2 boundary). |ΔΔG| = 1.64 — close to Cat 2. AlphaMissense 0.574 + Cataract 41 confirm pathogenic consequence.

Mechanism is volume mismatch in TM3 plus disruption of TM2-TM3 cross-helix contact (S353). Therapeutic strategy: TM2-TM3 interface site-directed design — same target as F350I.

Why this matters

V415F + F350I both touch the S353/S418 TM2-TM3 interface — two variants converge on this previously-unidentified cross-helix target.
Therapeutic Strategy Handoff · prediction

Feed this card to Wolfram Intelligence

Download the V415F PDF below and upload it to Wolfram Intelligence to generate therapeutic-strategy proposals — guanidinium mimetics, sigma-1 agonist docking, NAC thiol-capping. NAC is already on the bench-testing list.

Download V415F PDF card ↓Strategies are AI-generated predictions, not validated therapeutics.

UniProt Domain Annotation

Chain1890 · Wolframin
Transmembrane402422 · Helical
Natural variant415415 · in WFS1; greatly reduces protein expression compared to wild-type