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V412A

Category 4 — Stable Fold, Function DisruptedConflictingTransmembrane · predictedEditorial
ValineAlanine at position 412 · TM3 (402-422), helical transmembrane · WFS1 (Wolframin)

Valine → Alanine at position 412 inside TM3. ClinVar Conflicting including WFS1 spectrum. AlphaMissense 0.395 (below threshold), ΔΔG -1.23. Same position as V412L — second substitution at 412.

Interactive 3D Structure

Wild-type reference
Wild-type V412 — hydrogen bond to F408
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DynaMut2 mutant · V412A
Mutant A412 — hydrogen bond to M357 lost (6 contacts lost)
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Bond changes · DynaMut2 interaction analysis

6 lost1 gained12 preserved
Interaction typeWild-type partnerMutant partnerStatus
Hydrogen bondM357M357Preserved
Hydrogen bondF408F408Preserved
Hydrogen bondL409L409Preserved
Hydrogen bondV415V415Preserved
Hydrogen bondI416I416Preserved
Polar contactM357Lost
Polar contactF408F408Preserved
Polar contactL409L409Preserved
Polar contactF414Lost
Polar contactV415V415Preserved
Polar contactI416I416Preserved
Van der WaalsF408Lost
Van der WaalsL410Gained
Van der WaalsF414Lost
Van der WaalsI416I416Preserved
HydrophobicM357M357Preserved
HydrophobicF408Lost
HydrophobicI416Lost
HydrophobicM539M539Preserved

Lost / gained / preserved interatomic contacts at the variant residue, from the DynaMut2 (Arpeggio) interaction analysis of the wild-type and energy-minimized mutant structures.

Computational Predictions

DynaMut2 ΔΔG
-1.23kcal/mol
Destabilising — moderate
AlphaMissense
0.395
Amb
AlphaFold pLDDT
94
model confidence
Schema
Cat 4
Category 4 — Stable Fold, Function Disrupted

Clinical Evidence

ClinVar classificationConflicting classifications of pathogenicity
Review statuscriteria provided, conflicting classifications
Associated conditionsWFS1-Related Spectrum Disorders
InheritanceWFS1 spectrum.
Population frequency (gnomAD v4)Low frequency · AF 0.026%
cDNA changec.1235T>C
ClinVar accessionVCV000215387
Last evaluated2026/01/22 00:00

Observed in the general population.

Structural Context

Position 412 same neighbors as V412L: PHE413 (2.5 Å), SER411 (2.5 Å), LEU409 (3.8 Å), PHE408 (3.9 Å — TM3-TM7 interface position).

V412A is the more drastic substitution at 412 (vs the conservative V412L). Volume loss creates cavity in TM3. The F408 cross-helix contact is perturbed. |ΔΔG| 1.23 substantial. AM 0.395 below threshold but WFS1 spectrum confirms pathogenicity.

Amino-acid chemistry
Valine (V) → Alanine (A) — branched aliphatic replaced by small methyl-bearing. Volume decrease.
Position in the protein
TM3 (residues 402–422) · position 412 (pLDDT 94).

Druggability Assessment

Category 3/4 — Most Druggable (AM under-call). |ΔΔG| 1.23 substantial. AlphaMissense 0.395 below threshold but WFS1 spectrum + ΔΔG confirm pathogenicity.

Mechanism: cavity creation in TM3 + F408 cross-helix disruption. Therapeutic: same TM3-TM7 interface as V412L.

Why this matters

V412A + V412L at same position. Both AM under-calls; both target TM3-TM7 interface at F408.
Therapeutic Strategy Handoff · prediction

Feed this card to Wolfram Intelligence

Download the V412A PDF below and upload it to Wolfram Intelligence to generate therapeutic-strategy proposals — guanidinium mimetics, sigma-1 agonist docking, NAC thiol-capping. NAC is already on the bench-testing list.

Download V412A PDF card ↓Strategies are AI-generated predictions, not validated therapeutics.

UniProt Domain Annotation

Chain1890 · Wolframin
Transmembrane402422 · Helical